Small patella syndrome – A case report with review of literature

Vol 41 | Issue 1 | Jan-Jun 2020 | page: 32-34 | Kishore Chandra Das, Satya Ranjan Patra, Hemanta Kumar Bamidi, Siddhartha Shankar Mohanty


Authors: Kishore Chandra Das [1], Satya Ranjan Patra [1], Hemanta Kumar Bamidi [1], Siddhartha Shankar Mohanty [1]

[1] Department of Orthopaedics, Hi-Tech Medical College, Bhubaneswar, Odisha India.

Address of Correspondence
Dr. Satya Ranjan Patra,
Hi-Tech Medical College, Bhubaneswar, Odisha India.
E-mail: drsatyarp@gmail.com


Abstract

Small patella syndrome (SPS) or Hypoplastic patella syndrome (HPS) is a rare autosomal dominant disorder due to mutations in the TBX4 gene, characterized by the absence or hypoplasia of the patella with various anomalies of the pelvis and feet. We describe a case of a patient with hypoplastic patella of both knees presenting with pain and difficulty in walking; he was managed conservatively with non-steroidal anti-inflammatory drugs and an extension brace for three weeks followed by physiotherapy focusing on range of motion and quadriceps strengthening exercise.
Keywords: Small patella syndrome, Hypoplasia, Nail-patella syndrome, Patella aplasia-hypoplasia, Ischiopatella dysplasia, Ischio-pubic-patella syndrome or Scott-Taor syndrome, Hypoplastic patella syndrome, Ischiopubic synchondrosis


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How to Cite this Article: Das K C, Patra S R, Bamidi H K, Mohanty S S. | Small patella syndrome – A case report with review of literature. | Odisha Journal of Orthopaedics & Trauma | Jan-June 2020; 41(1): 32-34 .

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